Pradhan Pradeep, Samal Swagatika, Preetam C, Parida Pradipta
1Department of ENT and Head Neck Surgery, All India Institute of Medical Sciences, Bhubaneswar, Odisha 751019 India.
2Department of Pathology and Laboratory Medicine, All India Institute of Medical Sciences, Bhubaneswar, Odisha 751019 India.
Indian J Otolaryngol Head Neck Surg. 2019 Nov;71(Suppl 2):1217-1220. doi: 10.1007/s12070-018-1277-8. Epub 2018 Feb 19.
Paraganglioma is a rare benign tumour accounts for 0.6% of the all the malignancies affecting the head neck region. They originate from the paraganglionic cells from neuroendocrine tissues from skull base to the pelvic floor. Very rarely, temporal bone gets involved by the disease and it is the middle ear and mastoid complex which gets affected by the disease. Isolated involvement of the external auditory canal without the involvement of the tympanomastoid region is very unusual and only 5 cases have been reported in the literature till date. Again, coexisting middle ear disease with the canal paraganglioma is very rare and always being a challenge for the diagnosis due to its atypical presentation and its histopathogical features. Here, we present an atypical case of an external auditory canal paraganglioma, masquerading as complicated chronic otitis media.
副神经节瘤是一种罕见的良性肿瘤，占影响头颈部所有恶性肿瘤的0.6%。它们起源于从颅底到盆底神经内分泌组织的副神经节细胞。颞骨很少受累于该疾病，而中耳和乳突复合体是受该疾病影响的部位。外耳道单独受累而鼓室乳突区未受累非常罕见，迄今为止文献中仅报道了5例。此外，外耳道副神经节瘤合并中耳疾病非常罕见，由于其非典型表现和组织病理学特征，诊断始终具有挑战性。在此，我们报告一例伪装成复杂性慢性中耳炎的外耳道副神经节瘤非典型病例。
