Zografos Panagiotis M, Protopapas Eleftherios M, Hakim Nikolaos I, Alexopoulos Chrysanthos, Sarris George E
Athens Heart Surgery Institute, Iaso Children's Hospital, Athens, Greece.
Department of Pediatric Cardiac Anesthesiology and Intensive Care Unit, Ιaso Children's Hospital, Athens, Greece.
World J Pediatr Congenit Heart Surg. 2020 Jan;11(1):117-119. doi: 10.1177/2150135119878703. Epub 2019 Nov 22.
Aortopulmonary window (APW) is an abnormal congenital connection between the main pulmonary artery (MPA) and the ascending aorta, with intact aortic and pulmonary valves, leading to heart failure or, if not repaired early, to pulmonary vascular obstructive disease. We report the rare case of an asymptomatic adult with an unrestrictive APW, whose pulmonary arterial hypertension was remarkably still reversible, permitting successful repair.
主肺动脉窗(APW)是主肺动脉(MPA)与升主动脉之间一种异常的先天性连接,主动脉瓣和肺动脉瓣完整,可导致心力衰竭,若不及早修复,则会导致肺血管阻塞性疾病。我们报告了一例罕见的无症状成年患者,其主肺动脉窗无限制,肺动脉高压仍具有显著的可逆性,从而得以成功修复。