Department of Paediatric Cardiac Sciences, Sri Sathya Sai Sanjeevani Hospital, Raipur, Chhattisgarh, India.
Biosciences Institute, Faculty of Medical Sciences, Newcastle University, Newcastle upon Tyne, United Kingdom.
World J Pediatr Congenit Heart Surg. 2021 Nov;12(6):785-787. doi: 10.1177/2150135120957947. Epub 2021 May 10.
The association of total anomalous pulmonary venous connection (TAPVC) with aortopulmonary window (APW) is extremely rare. The coexistence of these two anomalies will have implications on clinical presentation, diagnosis, and pathophysiology. The lungs are exposed to pulmonary venous hypertension due to obstructed TAPVC as well as pulmonary arterial hypertension due to unrestrictive APW. We describe successful management of this unusual association in a three-month-old child.
完全性肺静脉异常连接(TAPVC)与主-肺动脉窗(APW)的关联极为罕见。这两种异常的共存将对临床表现、诊断和病理生理学产生影响。由于 TAPVC 受阻,肺部会受到肺静脉高压的影响,而由于 APW 不受限制,肺部会受到肺动脉高压的影响。我们描述了一例三个月大的婴儿中这种不常见关联的成功治疗。