Khanna Sudhansoo, Mahajan Sachin, Halder Vikram, Gowda Nischitha
Department of Cardiovascular and Thoracic Surgery, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India.
Department of Anaesthesia and Intensive Care, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India.
J Card Surg. 2020 Jun;35(6):1364-1367. doi: 10.1111/jocs.14569. Epub 2020 Apr 19.
Aortopulmonary window (APW) is a rare congenital cardiac condition. A large number of patients with a large APW usually die within 1 year of age. It is extremely rare to find cases of APW surviving till adult age and it is still rare to surgically treat such patients who are incidentally detected in adult age because such subsets of patients invariably have associated pulmonary vascular obstructive disease in advanced stage and thus there is therapeutic dilemma to surgically correct these patients. Although cases of uncorrected AP window presenting in adulthood have been reported but literature on surgically treated AP window in adult populations is limited. We describe case of APW in a 26-year-old male patient who was diagnosed incidentally while suspecting infective endocarditis and was subsequently surgically closed successfully with polytetrafluoroethylene patch after confirming reversibility of pulmonary arterial hypertension which is the key for successful outcome.
主肺动脉窗(APW)是一种罕见的先天性心脏疾病。大量患有大的主肺动脉窗的患者通常在1岁内死亡。极少能发现主肺动脉窗患者存活至成年,而在成年期偶然发现此类患者并进行手术治疗的情况仍然罕见,因为这类患者群体总是伴有晚期肺血管阻塞性疾病,因此在手术矫正这些患者时存在治疗困境。尽管有关于成年期未矫正主肺动脉窗病例的报道,但关于成年人群体中接受手术治疗的主肺动脉窗的文献有限。我们描述了一名26岁男性主肺动脉窗患者的病例,该患者在怀疑感染性心内膜炎时偶然被诊断出来,在确认肺动脉高压可逆性(这是成功治疗的关键)后,随后用聚四氟乙烯补片成功进行了手术闭合。