Björkman Patrick, Kantonen Ilkka, Blomqvist Carl, Venermo Maarit, Albäck Anders
Department of Vascular Surgery, Abdominal Center, Helsinki University Hospital, Helsinki, Finland.
Comprehensive Cancer Center, Helsinki University Hospital, Helsinki, Finland.
J Vasc Surg Cases Innov Tech. 2019 Nov 26;5(4):589-592. doi: 10.1016/j.jvscit.2019.08.002. eCollection 2019 Dec.
Aortic sarcomas have not been linked to Lynch syndrome in humans, although other soft tissue malignancies have been. We report the case of a 31-year-old man with Lynch syndrome, who presented with abdominal pain and severe claudication. The clinical and diagnostic workup revealed near occlusion of the infrarenal aorta due to aortic angiosarcoma. En bloc resection of the visceral and infrarenal aorta with right nephrectomy was performed, facilitated by temporary extracorporeal bypass to the visceral arteries. The aorta was reconstructed with a bifurcated Dacron graft. At the 24-month follow-up examination, the patient was free of disease but was experiencing chronic diarrhea.
主动脉肉瘤在人类中尚未与林奇综合征相关联，尽管其他软组织恶性肿瘤已被证实有关。我们报告了一例患有林奇综合征的31岁男性病例，该患者表现为腹痛和严重间歇性跛行。临床和诊断检查发现，由于主动脉血管肉瘤，肾下腹主动脉几乎闭塞。在内脏动脉临时体外旁路的辅助下，进行了内脏和肾下腹主动脉整块切除及右肾切除术。主动脉用分叉涤纶移植物重建。在24个月的随访检查中，患者无疾病，但仍有慢性腹泻。
