Pickford R W, Bose J, Joardar B S, Sen R N
Br J Physiol Opt. 1979;33(3):1-10.
As an exploratory study six colour vision tests were given to nine male and two female achromats from the Shankhabanik community in Bishnupur, and to two additional similar males. All thirteen subjects had severe photophobia, fixation nystagmus, extreme weakness of vision (4/24 to 3/60) and the red end of the spectrum was much shortened. This research indicates that they had a form of incomplete achromatopsia, varying from an almost complete to a very severe partial loss of colour vision. The condition is inherited as an autosomal recessive. The most likely interpretation of these cases is that they are incomplete rod achromats. Their performance on the colour vision tests is tabulated, and shows complete inability to do the Ishihara test; nearly complete inability on the HRR test, with a possible slight tendency to do better in the yellow-blue than the red-green sub-tests; on Sloan's test they show approximate accordance with her results for achromats; they have severe difficulty with the dichotomous and 100-hue tests, with a possible slight tendency to make fewer errors on the G/B sections. The anomaloscope shows little abnormality of mid-matching points, but great increases in average matching ranges above the normal, although not absolute loss of colour sense, but with extreme darkening or shortening of the red end of the spectrum. Their colour naming was carefully recorded, and was fairly good occasionally, sometimes erroneous without being wildly at fault, and most often completely wrong. The records of colour naming were made, not, of course, as a form of colour vision test, but simply to illustrate the ways in which such defectives make an effort to use colour names in general use among their friends and relatives.
作为一项探索性研究,对来自比什努布尔尚卡巴尼克社区的9名男性和2名女性全色盲患者,以及另外2名类似的男性进行了6项色觉测试。所有13名受试者都有严重的畏光、注视性眼球震颤、极度视力低下(4/24至3/60),并且光谱的红色端大大缩短。这项研究表明,他们患有某种形式的不完全性全色盲,从几乎完全丧失到非常严重的部分色觉丧失不等。这种病症以常染色体隐性方式遗传。对这些病例最可能的解释是,他们是不完全性视杆细胞全色盲患者。他们在色觉测试中的表现被制成表格,结果显示他们完全无法完成石原氏测试;在HRR测试中几乎完全无法完成,在黄蓝子测试中可能比红绿子测试表现稍好;在斯隆测试中,他们的表现与她对全色盲患者的测试结果大致相符;他们在二色性和100色调测试中困难重重,在G/B部分可能有稍微少犯错误的倾向。色盲检查镜显示中间匹配点几乎没有异常,但平均匹配范围比正常情况大幅增加,虽然不是完全丧失色觉,但光谱红色端极度变暗或缩短。他们的颜色命名被仔细记录下来,偶尔相当不错,有时有错误但不至于离谱,最常见的情况是完全错误。颜色命名记录当然不是作为一种色觉测试形式,而只是为了说明这些有缺陷的人在努力使用他们朋友和亲戚普遍使用的颜色名称的方式。