Zbeidy Reine, Torres Buendia Nathalia, Souki Fouad G
Anesthesiology, University of Miami School of Medicine, Miami, Florida, USA
Anesthesiology, University of Miami School of Medicine, Miami, Florida, USA.
BMJ Case Rep. 2020 Jan 23;13(1):e232964. doi: 10.1136/bcr-2019-232964.
Spondylothoracic dysostosis is a rare congenital disorder characterised by multiple vertebral malformations, shortening of the spine and fusion of the ribs at the costovertebral junction. These abnormalities create anaesthetic challenges due to difficult airway, severe restrictive lung disease and spine deformity necessitating a multidisciplinary approach and careful perioperative planning. We present the perianaesthetic management of a parturient with spondylothoracic dysostosis who successfully underwent preterm caesarean delivery under general anaesthesia with awake videolaryngoscopy-assisted tracheal intubation.
脊椎胸廓发育不良是一种罕见的先天性疾病,其特征为多个椎体畸形、脊柱缩短以及肋骨在肋椎关节处融合。由于气道困难、严重的限制性肺病和脊柱畸形,这些异常情况给麻醉带来了挑战,需要多学科方法和精心的围手术期规划。我们介绍了一位患有脊椎胸廓发育不良的产妇的围麻醉管理情况,该产妇在全身麻醉下行清醒视频喉镜辅助气管插管,成功进行了早产剖宫产。