Escoda T, Seguier J, Swiader L, Briantais A, Sampo M, Harlé J R, Durand J M
Service de médecine Interne, hôpital La Timone, Assistance publique, hôpitaux de Marseille, Aix-Marseille université, 13005 Marseille, France.
Service d'ophtalmologie, hôpital La Timone, Assistance publique, hôpitaux de Marseille, Aix-Marseille université, 13005 Marseille, France.
Rev Med Interne. 2020 Apr;41(4):279-283. doi: 10.1016/j.revmed.2019.12.024. Epub 2020 Jan 23.
Putscher-like retinopathy is a retinal disease that is similar to the syndrome initially described in 1910 by Purtscher, but occurring in a non-traumatic context.
We describe a case of acute, Putscher-like retinopathy in a 48-year-old woman experiencing adult onset Still's disease. The diagnosis was based on fundus examination and fluorescein angiography. Based on a review of the literature, we discuss the current available data on the pathophysiology of this syndrome and its prognostic significance. The treatment remains controversial.
When visual functional signs appear during adult Still's disease, it is necessary to evoke Putscher-like retinopathy, and to ask for an ophthalmological expertise.
类普舍尔视网膜病变是一种视网膜疾病,类似于1910年由普舍尔最初描述的综合征,但发生在非创伤性背景下。
我们描述了一例48岁患有成人斯蒂尔病的女性急性类普舍尔视网膜病变。诊断基于眼底检查和荧光素血管造影。基于文献回顾,我们讨论了关于该综合征病理生理学及其预后意义的现有数据。治疗仍存在争议。
当成人类斯蒂尔病出现视觉功能体征时,有必要考虑类普舍尔视网膜病变,并寻求眼科专业意见。