a Department of Ophthalmology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
b Department of Infectious Diseases and Clinical Microbiology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Ocul Immunol Inflamm. 2018;26(2):286-291. doi: 10.1080/09273948.2016.1213857. Epub 2016 Sep 6.
Adult-onset Still's disease (AOSD) is a rare multisystemic immune-mediated disease of unknown etiology with quotidian spiking fever, evanescent rash, arthralgia, and multiple organ involvement. The few AOSD cases that have been reported developed Purtscher's-like retinopathy associated with thrombotic microangiopathy (TMA). Here, we report Purtscher's-like retinopathy without TMA in a patient with AOSD. A 29-year-old-man who presented for evaluation of blurred vision was diagnosed with AOSD based on Yamaguchi criteria. He had Purtscher's-like retinopathy in his right eye. Lesions improved after steroid treatment. Although almost all reported AOSD cases with Purtscher's-like retinopathy are associated with TMA, in this case such a complication was not encountered.
成人Still 病(AOSD)是一种罕见的病因不明的多系统免疫介导性疾病,具有每日发热、一过性皮疹、关节炎和多器官受累。少数报道的 AOSD 病例发生与血栓性微血管病(TMA)相关的舒伯特样视网膜病变。在此,我们报告一例 AOSD 患者出现无 TMA 的舒伯特样视网膜病变。一名 29 岁男性因视力模糊就诊,根据 Yamaguchi 标准诊断为 AOSD。他的右眼患有舒伯特样视网膜病变。类固醇治疗后病变改善。虽然几乎所有报道的 AOSD 病例伴舒伯特样视网膜病变均与 TMA 相关,但在本例中未发生此类并发症。