Liu Feng-Cheng, Chiang Shang-Yi, Chang Deh-Ming, Lai Jenn-Haung, Hou Tsung-Yun, Chen Chen-Hung
Division of Rheumatology/Immunology/Allergy, Tri-Service General Hospital, National Defense Medical Center, Taipei, Taiwan, Republic of China.
Clin Rheumatol. 2007 Jul;26(7):1204-6. doi: 10.1007/s10067-006-0345-8. Epub 2006 Aug 10.
Adult-onset Still's disease is a multisystem inflammatory disorder of unknown etiology and is characterized by high, spiking fever, arthritis, evanescent maculopapular rash, myalgia, serositis, leukocytosis, and involvement of various organs including the eyes. The ocular manifestations have been described including orbital pseudotumor, ptosis, and diplopia with orbital pain but never Purtscher's-like retinopathy. We describe a 21-year-old male patient with adult-onset Still's disease who developed the Purtscher's-like retinopathy. To our knowledge, this is the first reported adult-onset Still's disease patient with Purtscher's-like retinopathy as the initial presentation.
成人斯蒂尔病是一种病因不明的多系统炎症性疾病，其特征为高热、弛张热、关节炎、一过性斑丘疹、肌痛、浆膜炎、白细胞增多以及包括眼睛在内的各种器官受累。已经描述过其眼部表现，包括眼眶假瘤、上睑下垂和伴有眼眶疼痛的复视，但从未有过类似Purtscher样视网膜病变的报道。我们描述了一名21岁患有成人斯蒂尔病的男性患者，该患者出现了类似Purtscher样视网膜病变。据我们所知，这是首例以类似Purtscher样视网膜病变为首发表现的成人斯蒂尔病患者。
