Tiwari Atul, Yadav Mohan L
Department of Pathology, Mahatma Gandhi Medical College & Hospital, Jaipur, IND.
Cureus. 2019 Dec 31;11(12):e6521. doi: 10.7759/cureus.6521.
Melanotic neuroectodermal tumor of infancy (MNTI) is a rare pigmented neoplasm of neural crest origin that most commonly arises in the maxilla of neonates and infants during the first year of life. We report the case of a three-month-old female child who presented with a 15-day history of intraoral swelling. Radiologically, the tumor was detected in the right maxilla, which was removed by wide local excision. Histopathological examination revealed the biphasic population of cells with melanin pigment deposition. Immunohistochemistry study was done confirming the diagnosis of MNTI.
婴儿黑色素性神经外胚层肿瘤（MNTI）是一种罕见的起源于神经嵴的色素性肿瘤，最常见于新生儿和1岁以内婴儿的上颌骨。我们报告一例3个月大女童，有15天的口腔内肿胀病史。影像学检查发现肿瘤位于右上颌骨，通过广泛局部切除将其切除。组织病理学检查显示有含黑色素沉着的双相细胞群。进行了免疫组织化学研究，确诊为MNTI。
