Oe Yukimura, Godai Kohei, Masuda Mina, Kanmura Yuichi
Department of Anesthesiology and Critical Care Medicine, Graduate School of Medical and Dental Sciences, Kagoshima University, 8-35-1 Sakuragaoka, Kagoshima, 890-8520, Japan.
JA Clin Rep. 2018 Feb 23;4(1):20. doi: 10.1186/s40981-018-0158-1.
Pallister-Hall syndrome is a rare disorder characterized by hypothalamic hamartoma, hypopituitarism, bifid epiglottis, and micrognathia.
We describe the airway management under general anesthesia of a 15-year-old female with Pallister-Hall syndrome whose airway was compromised with bifid epiglottis and acquired subglottic stenosis. The three options considered for airway management were tracheal intubation, a supraglottic device, and surgical tracheotomy. Tracheal intubation provides a secured airway, but extubation can be difficult. A supraglottic device minimizes airway injury, but it does not completely protect the airway from aspiration.
The patient's airway was successfully managed using a supraglottic device with aspiration prophylaxis. Airway management devices should be selected according to each patients' individual circumstances.
帕利斯特-霍尔综合征是一种罕见的疾病，其特征为下丘脑错构瘤、垂体功能减退、会厌裂和小颌畸形。
我们描述了一名患有帕利斯特-霍尔综合征的15岁女性在全身麻醉下的气道管理情况，该患者的气道因会厌裂和后天性声门下狭窄而受损。气道管理考虑的三种选择是气管插管、声门上装置和外科气管切开术。气管插管可确保气道安全，但拔管可能困难。声门上装置可将气道损伤降至最低，但不能完全防止气道误吸。
使用具有预防误吸功能的声门上装置成功管理了该患者的气道。应根据每个患者的具体情况选择气道管理装置。
