Chaves-Markman Ândrea, Markman Manuel, Santos-Veloso Marcelo Antônio O, Bezerra Lucas S, Sobral Filho Dário C, Markman Filho Brivaldo
Cardiology, Rarus - A Rare Disease Service, Recife, BES.
Echocardiography, Agamenon Magalhães Hospital, Recife, BRA.
Cureus. 2020 Jan 1;12(1):e6530. doi: 10.7759/cureus.6530.
Familial hypertrophic cardiomyopathy is an autosomal dominant genetic disease considered the most common cause of sudden cardiac death in individuals under 35 years old, especially the athletes. This study aimed to investigate the association between the presence of late potentials and a family history of sudden death, syncope, and complex ventricular arrhythmias on patients with hypertrophic cardiomyopathy. A case series study was carried out from March 2001 to December 2002, including 22 patients with hypertrophic cardiomyopathy according to transthoracic echocardiogram criteria. Patients on a cardiac pacemaker, right bundle branch block, cardiac transplant, and under no possibilities to realize the exams were excluded. The results showed that asymmetric septal hypertrophy was the most common type (73%), 63% had a positive familial history of hypertrophic cardiomyopathy, 55% sudden cardiac death, and 23% syncope. Also, complex ventricular arrhythmias were detected in 14% and late potentials in 23% of patients. According to this study, the presence of late potentials was not associated with familial sudden death, syncope, and complex ventricular arrhythmias.
家族性肥厚型心肌病是一种常染色体显性遗传病,被认为是35岁以下人群,尤其是运动员心脏性猝死的最常见原因。本研究旨在调查肥厚型心肌病患者中晚期电位的存在与猝死、晕厥及复杂性室性心律失常家族史之间的关联。2001年3月至2002年12月开展了一项病例系列研究,根据经胸超声心动图标准纳入22例肥厚型心肌病患者。排除了植入心脏起搏器、右束支传导阻滞、心脏移植患者以及无法进行相关检查的患者。结果显示,不对称性室间隔肥厚是最常见类型(73%),63%患者有肥厚型心肌病家族史阳性,55%有心脏性猝死家族史,23%有晕厥家族史。此外,14%的患者检测到复杂性室性心律失常,23%的患者检测到晚期电位。根据本研究,晚期电位的存在与家族性猝死、晕厥及复杂性室性心律失常无关。