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面肩肱型肌营养不良症:面部肌肉震颤

Facioscapulohumeral dystrophy: jitter in facial muscles.

作者信息

Trontelj J V, Zidar J, Denislic M, Vodusek D B, Mihelin M

机构信息

University Institute of Clinical Neurophysiology, University Medical Centre of Ljubljana, Yugoslavia.

出版信息

J Neurol Neurosurg Psychiatry. 1988 Jul;51(7):950-5. doi: 10.1136/jnnp.51.7.950.

DOI:10.1136/jnnp.51.7.950
PMID:3204404
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1033200/
Abstract

Motor end plate jitter was studied by single fibre EMG in the orbicularis oculi muscle of eight patients with facioscapulohumeral dystrophy activated by extramuscular nerve stimulation. The jitter was found to be slightly larger in comparison with the normal controls, although still within the normal limits in each patient. The findings are considered to indicate absence of any significant neuromuscular transmission disturbance, inflammatory or regenerative process, or reinnervation in progress. There was no evidence of muscle fibre conduction abnormality even in very weak muscle.

摘要

通过对8例面肩肱型肌营养不良患者眼轮匝肌进行肌外神经刺激激活后,采用单纤维肌电图研究运动终板颤抖。与正常对照组相比,发现颤抖略大,尽管每位患者仍在正常范围内。这些发现被认为表明不存在任何明显的神经肌肉传递障碍、炎症或再生过程,或正在进行的再支配。即使在非常弱的肌肉中,也没有肌肉纤维传导异常的证据。

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本文引用的文献

1
The neurogenic scapulo-peroneal syndrome.神经源性肩胛-腓骨综合征
Eur Neurol. 1968;1(5):257-74. doi: 10.1159/000113668.
2
Polymyositis with facioscapulohumeral distribution.面肩肱型分布的多发性肌炎。
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Axonal stimulation for end-plate jitter studies.用于终板肌电图研究的轴突刺激
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Adult onset scapuloperoneal myopathy.成人起病性肩胛腓骨肌病
J Neurol Neurosurg Psychiatry. 1975 Oct;38(10):1008-15. doi: 10.1136/jnnp.38.10.1008.
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Single fibre electromyography in various processes affecting the anterior horn cell.
J Neurol Sci. 1975 Apr;24(4):403-15. doi: 10.1016/0022-510x(75)90166-5.
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Jittermeter--a microcomputer-based system for single fibre electromyography.
Int J Biomed Comput. 1979 Nov;10(6):451-9. doi: 10.1016/0020-7101(79)90027-8.