Eyileten Zeynep, İştar Hande, Gümüş Fatih, Fitoz Suat, Uysalel Adnan
Department of Cardiovascular Surgery, Medicine Faculty of Ankara University, Ankara, Turkey.
Department of Radiology, Medicine Faculty of Ankara University, Ankara, Turkey.
Turk Gogus Kalp Damar Cerrahisi Derg. 2019 Jun 14;27(3):403-406. doi: 10.5606/tgkdc.dergisi.2019.17811. eCollection 2019 Jul.
Total anomalous pulmonary venous connection is an uncommon congenital heart malformation with abnormal drainage of all pulmonary veins into the systemic venous system. Despite its very low incidence, it is usually a pediatric cardiac emergency and rarely allows survival into adulthood without surgical correction in infancy. Herein, we report one of the oldest cases from Turkey who was successfully operated for non-obstructive, supracardiac total anomalous pulmonary venous connection.
完全性肺静脉异位连接是一种罕见的先天性心脏畸形,所有肺静脉均异常引流至体静脉系统。尽管其发病率极低,但它通常是儿科心脏急症,若在婴儿期未经手术矫正,很少能存活至成年。在此,我们报告一例来自土耳其的年龄较大的病例,该病例成功接受了非梗阻性心上型完全性肺静脉异位连接手术。