Bhandarkar Ajay, Menon Architha, Kudva Ranjini, Pujary Kailesh
Department of Otorhinolaryngology , Kasturba Medical College, Manipal Academy of Higher Education Madhavnagar Manipal - 576104.
Department of Pathology, Kasturba Medical College, Manipal Academy of Higher Education Manipal.
Iran J Otorhinolaryngol. 2020 Jan;32(108):57-61. doi: 10.22038/ijorl.2019.38807.2280.
Rhabdomyosarcoma is the most frequently occurring intrusive soft tissue sarcoma in the pediatric age group. Orbit is the most common location for a pediatric rhabdomyosarcoma, but it can occur in the oral cavity, pharynx, face and neck in the descending order of incidence. Rhabdomyosarcoma in the ear is extremely rare.
A 5-year-old girl presented to the outpatient department of our tertiary care hospital with complaints of foul smelling, non-blood stained right ear discharge of one-month duration and deviation of angle of mouth to the left side of acute onset. Investigations revealed a diagnosis of embryonal rhabdomyosarcoma. Multimodal therapy was carried out, and the child was rendered disease-free after two years.
Embryonal rhabdomyosarcoma of the head and neck mimics chronic otitis media. Early diagnosis is essential to deliver prompt treatment and prevent locoregional spread and metastasis.
横纹肌肉瘤是儿童年龄组中最常见的侵袭性软组织肉瘤。眼眶是儿童横纹肌肉瘤最常见的发病部位，但也可按发病率由高到低依次发生于口腔、咽部、面部和颈部。耳部横纹肌肉瘤极为罕见。
一名5岁女孩因持续1个月的右耳恶臭、非血性耳漏以及急性发作的口角向左偏斜，就诊于我们三级护理医院的门诊部。检查确诊为胚胎型横纹肌肉瘤。进行了多模式治疗，两年后患儿疾病痊愈。
头颈部胚胎型横纹肌肉瘤易误诊为慢性中耳炎。早期诊断对于及时治疗、预防局部扩散和转移至关重要。
