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本文引用的文献

1
A mild form of dermatomyositis as a prodromal sign of lung adenocarcinoma: a case report.一种轻度皮肌炎作为肺腺癌前驱体征:一例报告
J Med Case Rep. 2016 Feb 6;10:34. doi: 10.1186/s13256-016-0816-8.
2
Implications in the difference of anti-Mi-2 and -p155/140 autoantibody prevalence in two dermatomyositis cohorts from Mexico City and Guadalajara.墨西哥城和瓜达拉哈拉两个皮肌炎队列中抗Mi-2和-p155/140自身抗体患病率差异的影响
Arthritis Res Ther. 2013 Apr 4;15(2):R48. doi: 10.1186/ar4207.
3
Clinical presentation and evaluation of dermatomyositis.皮肌炎的临床表现与评估
Indian J Dermatol. 2012 Sep;57(5):375-81. doi: 10.4103/0019-5154.100486.
4
Clinical correlations with dermatomyositis-specific autoantibodies in adult Japanese patients with dermatomyositis: a multicenter cross-sectional study.日本成年皮肌炎患者中皮肌炎特异性自身抗体的临床相关性:一项多中心横断面研究。
Arch Dermatol. 2011 Apr;147(4):391-8. doi: 10.1001/archdermatol.2011.52.
5
Expression of the dermatomyositis autoantigen Mi-2 in regenerating muscle.皮肌炎自身抗原Mi-2在再生肌肉中的表达。
Arthritis Rheum. 2009 Dec;60(12):3784-93. doi: 10.1002/art.24977.
6
UV radiation regulates Mi-2 through protein translation and stability.紫外线辐射通过蛋白质翻译和稳定性来调节Mi-2。
J Biol Chem. 2008 Dec 12;283(50):34976-82. doi: 10.1074/jbc.M805383200. Epub 2008 Oct 15.
7
The chromatin remodeler Mi-2beta is required for establishment of the basal epidermis and normal differentiation of its progeny.染色质重塑因子Mi-2β是基底表皮建立及其后代正常分化所必需的。
Development. 2007 Apr;134(8):1571-82. doi: 10.1242/dev.001750. Epub 2007 Mar 14.
8
A systematic review of adult-onset clinically amyopathic dermatomyositis (dermatomyositis siné myositis): a missing link within the spectrum of the idiopathic inflammatory myopathies.成人起病的临床无肌病性皮肌炎(无肌性皮肌炎)的系统评价:特发性炎性肌病谱系中的缺失环节
J Am Acad Dermatol. 2006 Apr;54(4):597-613. doi: 10.1016/j.jaad.2005.10.041. Epub 2006 Jan 23.
9
Anti-Mi-2 antibodies.抗Mi-2抗体
Autoimmunity. 2005 Feb;38(1):79-83. doi: 10.1080/08916930400022681.
10
Global surface ultraviolet radiation intensity may modulate the clinical and immunologic expression of autoimmune muscle disease.全球地表紫外线辐射强度可能会调节自身免疫性肌肉疾病的临床和免疫表现。
Arthritis Rheum. 2003 Aug;48(8):2285-93. doi: 10.1002/art.11090.

经典型皮肌炎:一例报告

Classical Dermatomyositis: A Case Report.

作者信息

Pokhrel Sushant, Pardhe Bashu Dev, Giri Nisha, Pokhrel Rakesh, Paudel Deliya

机构信息

Department of Laboratory Medicine, Manmohan Memorial Institute of Health Sciences, Kathmandu, Nepal.

Modern Diagnostic Laboratory and Research Center, Kathmandu, Nepal.

出版信息

Clin Cosmet Investig Dermatol. 2020 Feb 5;13:123-126. doi: 10.2147/CCID.S234452. eCollection 2020.

DOI:10.2147/CCID.S234452
PMID:32104038
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7008393/
Abstract

Dermatomyositis is an idiopathic myopathy involving progressive muscle weakness with skin manifestation. Diagnosis is based upon the progressive muscle weakness, skin rashes, elevated serum muscle enzymes, muscle biopsy, and abnormal electromyogram. The incidence of dermatomyositis is rare. In this case study, we report a case of classical dermatomyositis without incidence of malignancy. Timely diagnosis and administration of steroid led to better prognosis of the patient.

摘要

皮肌炎是一种特发性肌病,伴有进行性肌无力和皮肤表现。诊断基于进行性肌无力、皮疹、血清肌酶升高、肌肉活检及异常肌电图。皮肌炎的发病率很低。在本病例研究中,我们报告一例无恶性肿瘤发生的经典皮肌炎病例。及时诊断并给予类固醇治疗使患者预后较好。