Corbel L, Souissi M, Chrétien Y, Dufour B
Service d'Urologie, Hôpital Necker, Paris.
J Radiol. 1992 Dec;73(12):669-72.
Desmoid tumors are rare lesions with a local invasive potential and a risk of recurrence considered as benign due to the absence of metastases. They are included in fibromatoses and may be associated with Gardner's syndrome. The authors report an unusual case, in a 26 year old man, of a desmoid tumor invading ileon, right colon, appendix and the right ureter and responsible of a ureteral obstruction. Etiologic factors (traumatic, hormonal, auto-immune...) are discussed. The treatment of choice to lower the risk of recurrence is the complete surgical removal of the tumor.
硬纤维瘤是一种罕见的病变,具有局部侵袭性且有复发风险,因其无转移而被视为良性。它们被归入纤维瘤病,可能与加德纳综合征有关。作者报告了一例不寻常的病例,一名26岁男性患有硬纤维瘤,该肿瘤侵犯回肠、右结肠、阑尾和右输尿管,并导致输尿管梗阻。文中讨论了病因(创伤性、激素性、自身免疫性等)。降低复发风险的首选治疗方法是完整手术切除肿瘤。