Demir Ömer Faruk, Önal Ömer, Hasdıraz Leyla, Oğuzkaya Fahri, Kontaş Olgun, Ülgey Ayşe
Department of Thoracic Surgery, Erciyes University Faculty of Medicine, Kayseri, Turkey.
Department of Pathology, Erciyes University Faculty of Medicine, Kayseri, Turkey.
Turk Gogus Kalp Damar Cerrahisi Derg. 2020 Jan 23;28(1):209-212. doi: 10.5606/tgkdc.dergisi.2020.18215. eCollection 2020 Jan.
Pleuropulmonary blastoma is a rare and aggressive childhood tumor of mesenchymal origin. It has a poor prognosis and mainly classified as cystic (type 1), mixed type (type 2), and solid (type 3). Herein, we present two cases of pleuropulmonary blastoma type 3 presenting with pneumothorax, a rare clinical presentation of pleuropulmonary blastoma, which was successfully treated with surgery.
胸膜肺母细胞瘤是一种罕见的、具有侵袭性的间叶源性儿童肿瘤。其预后较差,主要分为囊性(1型)、混合型(2型)和实性(3型)。在此,我们报告两例3型胸膜肺母细胞瘤表现为气胸的病例,这是胸膜肺母细胞瘤一种罕见的临床表现,通过手术成功治愈。