Lehmann Carlos, Rodriguez Ossa Paola, Vargas Manrique Maria, Acosta Alvaro E, Quintero Pérez Yesid
Breast and Soft Tissue Surgery, National Cancer Institute, Bogotá D.C., COL.
Pathology, National Cancer Institute, Bogotá D.C., COL.
Cureus. 2020 Feb 4;12(2):e6873. doi: 10.7759/cureus.6873.
Eccrine porocarcinoma is a rare malignant tumor that develops in the eccrine glands, appearing as a primary tumor, or by malignant transformation of an eccrine poroma. It is a carcinoma with high metastatic and recurrent potential; it has the same incidence in both sexes, and mainly affects the elderly. Its diagnosis, rather than clinical, is histological, and due to the rarity of the disease, it is a pathological challenge. There are no standardized treatment guidelines for porocarcinoma, but surgical resection with tumor-free margins is considered the basis of treatment, in addition to sentinel node biopsy under risk factors and individualization of each patient. For the metastatic form, chemotherapy and radiotherapy are the treatment of choice. Herein, we present the case of a man with eccrine porocarcinoma with extensive zosteriform skin metastasis and lymph node involvement, treated with chemotherapy and concomitant radiotherapy.
小汗腺汗孔癌是一种罕见的恶性肿瘤,发生于小汗腺,可表现为原发性肿瘤,也可由小汗腺汗孔瘤恶变而来。它是一种具有高转移和复发潜能的癌;男女发病率相同,主要影响老年人。其诊断依靠组织学而非临床症状,由于该疾病罕见,它是一项病理学挑战。对于汗孔癌没有标准化的治疗指南,但除了在危险因素下进行前哨淋巴结活检及对每个患者进行个体化治疗外,具有切缘无瘤的手术切除被认为是治疗的基础。对于转移型,化疗和放疗是首选治疗方法。在此,我们报告一例患有广泛带状疱疹样皮肤转移和淋巴结受累的小汗腺汗孔癌男性患者,接受了化疗及同步放疗。