Afzal Zeeshan, Stupalkowska Weronika, Mahler-Araujo Maria B, Bowden David, Davies Richard J
Cambridge Colorectal Unit, Box 201, Addenbrooke's Hospital, Cambridge University Hospitals NHS Foundation Trust, Cambridge CB2 0QQ, UK.
Department of Histopathology, Box 235, Addenbrooke's Hospital, Cambridge University Hospitals NHS Foundation Trust, Cambridge CB2 0QQ, UK.
J Surg Case Rep. 2020 Mar 17;2020(3):rjaa045. doi: 10.1093/jscr/rjaa045. eCollection 2020 Mar.
Primary retroperitoneal mucinous cystadenoma (PRMC) is a rare tumour. It was first reported in 1965, and since then, less than 100 cases have been reported. It is cystic in nature and most commonly affects the female population. It becomes symptomatic in later stages due to its mass effect, making the diagnosis challenging in its early asymptomatic stage. We report a case of a 32-year-old female who presented with abdominal pain and a mass in left iliac fossa. Diagnostic imaging revealed a large cystic lesion in retroperitoneum. A midline laparotomy was performed, and a complete surgical excision was accomplished without any spillage. Surgical histology confirmed the diagnosis of PRMC. The patient was discharged on postoperative day 2. There was no evidence of tumour recurrence on repeat imaging at 90-day follow-up. Surgical approach, with complete resection and without any spillage, remains the most effective and appropriate treatment for this tumour.
原发性腹膜后黏液性囊腺瘤（PRMC）是一种罕见的肿瘤。它于1965年首次被报道，自那时起，报道的病例不到100例。其本质为囊性，最常累及女性人群。由于其占位效应，它在后期才会出现症状，这使得在早期无症状阶段进行诊断具有挑战性。我们报告一例32岁女性患者，她因腹痛和左下腹肿块就诊。诊断性影像学检查显示腹膜后有一个大的囊性病变。进行了中线剖腹手术，实现了完整的手术切除且无任何渗漏。手术组织学检查确诊为PRMC。患者术后第2天出院。90天随访时的重复影像学检查未发现肿瘤复发迹象。手术切除且无任何渗漏的手术方法仍然是治疗该肿瘤最有效且合适的方法。
