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酷似慢性肺血栓栓塞症的纤维性纵隔炎

Fibrosing mediastinitis mimicking as chronic pulmonary thromboembolism.

作者信息

Sinha Dimpi, Kundaragi Nischal G, Kale Sudhir Kumar, Sharma Sukrity

机构信息

Department of Radiology, Aster CMI Hospital, Bangalore, India.

Department of Interventinal Radiology, Aster CMI Hospital, Bangalore, India.

出版信息

BJR Case Rep. 2020 Feb 12;6(1):20190049. doi: 10.1259/bjrcr.20190049. eCollection 2020 Mar.

Abstract

Fibrosing mediastinitis is an uncommon, benign, progressive disorder caused by proliferation of fibrous tissue within mediastinum resulting in encasement of vital mediastinal broncho-vascular structures. Due to its rarity and variable clinical presentation, it is often misdiagnosed. We are presenting a case of fibrosing mediastinitis in an Ethiopian origin young male presenting with pulmonary hypertension due to simultaneous occlusion of pulmonary vein and arteries, clinically misdiagnosed as chronic pulmonary thromboembolism.

摘要

纤维性纵隔炎是一种罕见的、良性的、进行性疾病,由纵隔内纤维组织增生引起,导致重要的纵隔支气管血管结构被包裹。由于其罕见性和临床表现多样,常被误诊。我们报告一例来自埃塞俄比亚的年轻男性纤维性纵隔炎病例,该患者因肺静脉和动脉同时闭塞出现肺动脉高压,临床上被误诊为慢性肺血栓栓塞症。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fc5/7068094/80c3622f5a87/bjrcr.20190049.g001.jpg

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