Raffaelli P, Ronzini M F
Clinica Ortopedica dell'Università, Ancona.
Ital J Orthop Traumatol. 1988 Jun;14(2):267-71.
Camurati-Engelmann's syndrome is a rare congenital disease characterised by hyperostosis and sclerosis with a predilection for the long bones of the lower limbs. The authors report a case in an adult with a family history of the disease, and multiple localisations in the diaphyses of the long bones. The site of pain and greatest involvement of the disease was the right tibia and fibula. The affection was treated by drilling and reaming the medullary canal with drills of increasing diameter. This method is easy to carry out, causes little trauma, and has undoubted advantages in greatly reducing the period of bedrest and aiding functional recovery.
卡姆拉蒂 - 恩格尔曼综合征是一种罕见的先天性疾病，其特征为骨肥厚和骨质硬化，以下肢长骨受累为主。作者报告了一例有该疾病家族史的成年患者，其长骨干骺端有多处病变。疼痛部位及该疾病最严重的受累部位是右胫骨和腓骨。通过使用直径逐渐增大的钻头对髓腔进行钻孔和扩孔来治疗这种病症。这种方法易于实施，创伤小，在大幅缩短卧床休息时间和促进功能恢复方面具有毋庸置疑的优势。
