Byanyima Rosemary Kusaba, Nabawesi Jennifer Batuuka
Department of Radiology, Faculty of Medicine, P O Box 7072, Kampala, Uganda.
Afr Health Sci. 2002 Dec;2(3):118-20.
Camurati-Engelmann's disease is a rare condition worldwide. No cases have been documented in Uganda. A 26 year old female presented with a history of grinding pain in the limbs for over 20 years. Strong painkillers would temporally relieve the pain. She had an asthenic stature with generalised reduction in muscle bulk. Plain x-rays revealed the characteristic symmetrical thickening and sclerosis of the diaphyses of the appendicular skeleton and skull base, which is pathognomonic of Camurati-Engelmann's disease. Involvement of the metaphyses of these long bones as well as the metacarpal bones makes this an unusual case.
卡姆拉蒂-恩格尔曼病在全球范围内都很罕见。乌干达尚无相关病例记录。一名26岁女性,有超过20年的肢体隐痛病史。强效止痛药可暂时缓解疼痛。她身材虚弱,全身肌肉量减少。X线平片显示四肢骨骼和颅底骨干有特征性的对称性增厚和硬化,这是卡姆拉蒂-恩格尔曼病的特征性表现。这些长骨的干骺端以及掌骨受累,使得该病例较为特殊。