Sørensen T T
Department of Neurology, Central Hospital, Viborg, Denmark.
Acta Neurol Scand. 1988 Dec;78(6):542-3. doi: 10.1111/j.1600-0404.1988.tb03699.x.
Family cases of recurrent cranial nerve palsies are seldom reported. This paper presents a family with recurrent facial and ocular nerve palsies in 2 brothers. Their father and his sister had Bell's palsies. Examinations provided no explanation. Six previous reports of families with recurrent cranial nerve palsies are summarized. The pedigrees speak in favour of an autosomal dominant mode of inheritance of predisposing factors. The pathogenetic mechanism might be vascular or autoimmune, but is still unknown.
家族性复发性颅神经麻痹的病例鲜有报道。本文介绍了一个家族,该家族中有2名兄弟患有复发性面神经和眼神经麻痹。他们的父亲及其妹妹曾患贝尔氏麻痹。各项检查均未给出解释。本文总结了之前6例复发性颅神经麻痹家族的报告。这些系谱表明存在易患因素的常染色体显性遗传模式。发病机制可能是血管性或自身免疫性的,但仍不清楚。