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一例临床上表现为斯蒂尔-理查森-奥尔谢夫斯基综合征的进行性皮质下胶质增生症。

A case of progressive subcortical gliosis presenting clinically as Steele-Richardson-Olszewski syndrome.

作者信息

Will R G, Lees A J, Gibb W, Barnard R O

机构信息

Maida Vale Hospital for Nervous Diseases, London, UK.

出版信息

J Neurol Neurosurg Psychiatry. 1988 Sep;51(9):1224-7. doi: 10.1136/jnnp.51.9.1224.

DOI:10.1136/jnnp.51.9.1224
PMID:3225606
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1033033/
Abstract

A patient presenting with the characteristic clinical features of Steele-Richardson-Olszewski syndrome is described, in whom neuropathological examination revealed atypical features, including extensive cortical and subcortical gliosis. The clinical and pathological features are discussed with particular reference to Creutzfeldt-Jacob disease and it is proposed that the case should be classified as progressive subcortical gliosis.

摘要

本文描述了一名具有Steele-Richardson-Olszewski综合征典型临床特征的患者，其神经病理学检查显示出非典型特征，包括广泛的皮质和皮质下胶质增生。结合克雅氏病对临床和病理特征进行了讨论，并提出该病例应归类为进行性皮质下胶质增生。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/91ac/1033033/f4275e09f936/jnnpsyc00544-0113-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/91ac/1033033/75419dec1ad2/jnnpsyc00544-0113-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/91ac/1033033/f4275e09f936/jnnpsyc00544-0113-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/91ac/1033033/75419dec1ad2/jnnpsyc00544-0113-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/91ac/1033033/f4275e09f936/jnnpsyc00544-0113-b.jpg

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Progressive subcortical gliosis and progressive supranuclear palsy can have similar clinical and PET abnormalities.进行性皮质下胶质增生症和进行性核上性麻痹可具有相似的临床及PET异常表现。
J Neurol Neurosurg Psychiatry. 1992 Aug;55(8):707-13. doi: 10.1136/jnnp.55.8.707.
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Progressive subcortical gliosis, a rare form of presenile dementia.进行性皮质下胶质增生症，一种罕见的早老性痴呆形式。
Brain. 1967 Jun;90(2):405-18. doi: 10.1093/brain/90.2.405.
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