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急性心力衰竭作为嗜铬细胞瘤的首发表现并合并“反向” Takotsubo综合征

Acute Heart Failure as a First Presentation of Pheochromocytoma Complicated with "Inverted" Takotsubo Syndrome.

作者信息

Spapen Jerrold, de Filette Jeroen, Lochy Stijn, Spapen Herbert

机构信息

Department of Cardiology, Universitair Ziekenhuis Brussel, Brussels, Belgium.

Department of Endocrinology, Universitair Ziekenhuis Brussel, Brussels, Belgium.

出版信息

Case Rep Endocrinol. 2020 Mar 17;2020:2521046. doi: 10.1155/2020/2521046. eCollection 2020.

DOI:10.1155/2020/2521046
PMID:32257461
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7103034/
Abstract

Takotsubo syndrome is a rare but emerging form of acute reversible myocardial injury characterized by transient systolic LV dysfunction, often related to emotional or physical stress. Pheochromocytoma is increasingly recognised as another possible trigger. Pheochromocytoma is a rare catecholamine-secreting tumour arising from chromaffin cells within the adrenal medulla or extra-adrenal paraganglia. The pathognomonic quartet of paroxysmal hypertension, palpitations, headache, and diaphoresis is rarely present, and diagnosis is often delayed. We describe a 43-year-old formerly healthy patient with an adrenal pheochromocytoma, presenting as an "inverted" takotsubo syndrome complicated with acute heart failure and pulmonary oedema.

摘要

应激性心肌病是一种罕见但日益常见的急性可逆性心肌损伤形式,其特征为短暂的左心室收缩功能障碍,常与情绪或身体应激有关。嗜铬细胞瘤越来越被认为是另一种可能的诱因。嗜铬细胞瘤是一种罕见的分泌儿茶酚胺的肿瘤,起源于肾上腺髓质或肾上腺外副神经节内的嗜铬细胞。阵发性高血压、心悸、头痛和多汗这一典型四联征很少出现,诊断往往延迟。我们描述了一名43岁既往健康的患者,患有肾上腺嗜铬细胞瘤,表现为“倒转型”应激性心肌病并伴有急性心力衰竭和肺水肿。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/7103034/8bbaec4902d3/CRIE2020-2521046.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/7103034/734c4ee29718/CRIE2020-2521046.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/7103034/902282e39319/CRIE2020-2521046.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/7103034/8bbaec4902d3/CRIE2020-2521046.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/7103034/734c4ee29718/CRIE2020-2521046.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/7103034/902282e39319/CRIE2020-2521046.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/7103034/8bbaec4902d3/CRIE2020-2521046.003.jpg

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本文引用的文献

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Pheochromocytoma- and paraganglioma-triggered Takotsubo syndrome.儿茶酚胺细胞瘤和副神经节瘤引发的 Takotsubo 综合征。
Endocrine. 2019 Sep;65(3):483-493. doi: 10.1007/s12020-019-02035-3. Epub 2019 Aug 9.
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Eur Heart J. 2018 Jun 7;39(22):2047-2062. doi: 10.1093/eurheartj/ehy077.
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Pheochromocytoma Is Characterized by Catecholamine-Mediated Myocarditis, Focal and Diffuse Myocardial Fibrosis, and Myocardial Dysfunction.嗜铬细胞瘤的特征是儿茶酚胺介导的心肌炎、局灶性和弥漫性心肌纤维化以及心肌功能障碍。
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Life-threatening events in patients with pheochromocytoma.患者发生嗜铬细胞瘤危象。
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