Ahmed Talha, Safdar Ayesha, Ramani Gautam
Internal Medicine, University of Maryland, Baltimore, USA.
Internal Medicine, Army Medical College, Rawalpindi, PAK.
Cureus. 2020 Mar 8;12(3):e7212. doi: 10.7759/cureus.7212.
Restrictive cardiomyopathy (CM) usually develops and progresses slowly, over a course of years. The rapid development of idiopathic restrictive CM immediately following a liver transplant is unusual. We describe the case of a patient who developed idiopathic restrictive CM fairly rapidly following a liver transplant. It progressed within a few months to the point where the patient required scheduled paracenteses and dialysis. The morphological definition of restrictive CM consists of bi-atrial dilation with non-dilated and non-hypertrophic ventricles. A cardiac biopsy may be needed when the underlying cause is not evident. When a cardiac biopsy is not able to identify a specific cause, then the word "idiopathic" is used to describe the CM.
限制性心肌病（CM）通常在数年的病程中缓慢发展和进展。肝移植后立即快速发展的特发性限制性CM并不常见。我们描述了一例肝移植后相当迅速地发展为特发性限制性CM的患者。该病在几个月内进展到患者需要定期进行腹腔穿刺和透析的程度。限制性CM的形态学定义包括双房扩张，心室未扩张且无肥厚。当潜在病因不明显时，可能需要进行心脏活检。当心脏活检无法确定具体病因时，则使用“特发性”一词来描述CM。
