Catalano R A, Calhoun J H, Reinecke R D, Cogan D G
Department of Ophthalmology, Albany Medical Center Hospital, New York 12208.
Can J Ophthalmol. 1988 Dec;23(7):318-21.
A 10-month-old girl presented with apparently unilateral ocular motor apraxia (OMA). Electro-oculography confirmed an inability to generate a saccade for fixation or in response to an optokinetic or vestibular evoked stimulus to the right. Fixation and optokinetic saccades and vestibular evoked nystagmus were present to the left. Magnetic resonance imaging revealed a small cerebellar vermis but no localizing unilateral abnormality or tumour. Subsequent review of video recordings of 16 children with congenital OMA revealed that 5 demonstrated asymmetry in the generation of fixation saccades. Two of the five also demonstrated asymmetry of vestibular evoked nystagmus, and an additional child had optokinetic asymmetry.
一名10个月大的女孩表现出明显的单侧眼球运动失用症（OMA）。眼电图证实，她无法产生用于注视的扫视运动，也无法对向右的视动或前庭诱发刺激做出反应。向左的注视、视动性扫视运动和前庭诱发的眼球震颤均存在。磁共振成像显示小脑蚓部较小，但未发现定位性单侧异常或肿瘤。随后对16名先天性OMA患儿的视频记录进行回顾发现，5名患儿在产生注视性扫视运动时表现出不对称性。这5名患儿中有2名还表现出前庭诱发眼球震颤的不对称性，另有1名患儿存在视动不对称性。
