Ostuni P A, Lazzarin P, Ongaro G, Gusi R, Todesco S, Gambari P F
Division of Rheumatology, University of Padova, Italy.
Clin Rheumatol. 1988 Sep;7(3):398-401. doi: 10.1007/BF02239200.
We report a new case of hyper-IgD syndrome, a recently described disease characterized by recurrent episodes of fever with headache, bilateral cervical lymphadenopathy and, more rarely, abdominal pain and diarrhoea. Polyclonal increase of serum IgD is the most important laboratory finding. Etiopathogenesis and differences with familial Mediterranean fever are discussed. Moreover, good results obtained with colchicine treatment are also reported.
我们报告了一例高IgD综合征的新病例，这是一种最近描述的疾病，其特征为反复发热伴头痛、双侧颈部淋巴结病，较少见的有腹痛和腹泻。血清IgD的多克隆升高是最重要的实验室检查发现。本文讨论了其病因发病机制以及与家族性地中海热的区别。此外，还报告了秋水仙碱治疗取得的良好效果。
