Pasha Hamdan Ahmed, Ghaloo Shayan Khalid, Wasif Muhammad, Siddiqui Moghira Iqbaluddin, Din Nasir Ud
Department of Otorhinolaryngology-Head and Neck Surgery, Aga Khan University Hospital Karachi, Karachi, Pakistan.
Turk Arch Otorhinolaryngol. 2020 Mar;58(1):65-68. doi: 10.5152/tao.2020.4839. Epub 2020 Mar 26.
Ewing Sarcoma of the head and neck region is an extremely rare entity. Treatment usually involves surgery, chemotherapy and radiotherapy in varying sequences. We present the third case to date of Ewing sarcoma of the larynx in a paediatric population. A 5-year-old boy presented to emergency room with acute respiratory distress. Computerized tomography scan showed a mass in the supraglottis; he was intubated using videolaryngoscope and tracheostomy was avoided, mass was removed by cold dissection. Final histopathologic examination revealed Ewing sarcoma. Further workup showed no systemic metastasis. Patient was advised adjuvant therapy which the family refused. Currently he is doing fine on 2 years of follow-up.
头颈部尤因肉瘤是一种极为罕见的疾病。治疗通常包括以不同顺序进行的手术、化疗和放疗。我们报告了迄今为止儿科人群中第三例喉尤因肉瘤病例。一名5岁男孩因急性呼吸窘迫被送往急诊室。计算机断层扫描显示声门上区有一个肿块;使用视频喉镜对其进行插管,避免了气管切开术,通过冷剥离术切除了肿块。最终的组织病理学检查显示为尤因肉瘤。进一步检查未发现全身转移。建议患者进行辅助治疗,但家属拒绝了。目前,经过2年的随访,他情况良好。