Aghaei Moghadam Ehsan, Aslani Nahid, Mojtabavi Helia, Larti Farnoosh, Ghamari Azin, Ziaee Vahid
Department of Pediatrics, Tehran University of Medical Science, Tehran, Iran.
Children's Medical Center, Pediatrics Center of Excellence, Tehran, Iran.
Case Rep Cardiol. 2020 Apr 19;2020:3417910. doi: 10.1155/2020/3417910. eCollection 2020.
Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per million. Six percent of the affected cases have cardiac involvements; among which, aneurysms comprise the lowest penetrance. By this paper, we aim to cast light on clinical diagnostic and treatment methods of a rare case presentation, a 10-year-old male GPA patient, diagnosed with massive thrombosis at his coronary artery aneurysm. GPA should be considered as differential diagnosis of prolong fever and coronary aneurysms in adolescents.
肉芽肿性多血管炎(GPA)是一种中小血管的坏死性血管炎,传统上认为主要累及呼吸道,并伴有局灶性肾脏受累,其主要表现相对罕见,年发病率为每百万人口20 - 50例。6%的受累病例有心脏受累;其中,动脉瘤的发生率最低。在本文中,我们旨在阐明一例罕见病例的临床诊断和治疗方法,该病例为一名10岁男性GPA患者,被诊断为冠状动脉瘤内大量血栓形成。GPA应被视为青少年长期发热和冠状动脉瘤的鉴别诊断。