Desdiani Desdiani, Darifah Siti, Azali Chairul
Faculty of Medicine Sultan Ageng Tirtayasa University Cilegon Banten Indonesia.
Faculty of Medicine University of North Sumatera Megan Indonesia.
Respirol Case Rep. 2020 May 5;8(5):e00567. doi: 10.1002/rcr2.567. eCollection 2020 Jul.
Pulmonary malignant peripheral nerve sheath tumours (MPNSTs) are extremely rare soft tissue sarcomas that develop from the cell constituting the nerve sheaths, approximately 5-10% of all soft tissue sarcomas. We present a rare case of primary lung MPNST in an adult female non-smoker patient, in whom surgical thoracotomy approach has obtained a good control of the disease. Low-grade MPNST was established from excisional biopsy followed by immunohistochemistry.
肺恶性外周神经鞘瘤（MPNSTs）是极其罕见的软组织肉瘤，由构成神经鞘的细胞发展而来，约占所有软组织肉瘤的5%-10%。我们报告了一例成年非吸烟女性原发性肺MPNST的罕见病例，该患者通过手术开胸方法实现了对疾病的良好控制。通过切除活检及免疫组化确诊为低级别MPNST。
