Klingler Jan-Helge, Elsheikh Samer, Doostkam Soroush, Krüger Marie T, Blaß Bianca-Ioana, Steiert Christine
Department of Neurosurgery, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Germany.
Department of Neuroradiology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Germany.
J Clin Neurosci. 2020 Jul;77:217-221. doi: 10.1016/j.jocn.2020.05.025. Epub 2020 May 7.
A 20-year-old patient with a history of von Hippel-Lindau disease reported on thoracic back pain radiating to the left shoulder for 10 weeks. Magnetic resonance imaging revealed a progressive contrast-enhancing tumor (14 × 21 × 28 mm) compressing the spinal cord and extending into the left neural foramen at T5/6. After embolization of supplying vessels, the tumor was completely resected via hemilaminectomy of T5. The postoperative course was uneventful without surgery related morbidity. The pathological examination disclosed a paraganglioma WHO grade I. We discuss the differential diagnoses and pitfalls of this unexpected finding in this patient with von Hippel-Lindau disease.
一名患有冯·希佩尔-林道病的20岁患者报告称，其胸背部疼痛向左肩部放射，持续了10周。磁共振成像显示有一个进行性强化的肿瘤（14×21×28毫米），压迫脊髓并延伸至T5/6左侧神经孔。在对供血血管进行栓塞后，通过T5半椎板切除术将肿瘤完全切除。术后过程顺利，无手术相关并发症。病理检查显示为世界卫生组织I级副神经节瘤。我们讨论了该患有冯·希佩尔-林道病的患者这一意外发现的鉴别诊断及陷阱。
