Athyal R P, Al-Khawari H, Arun N, Abul F, Patrick J
Department of Clinical Radiology, Al Amiri Hospital, Kuwait.
Australas Radiol. 2007 Oct;51 Spec No.:B67-70. doi: 10.1111/j.1440-1673.2007.01758.x.
Pheochromocytoma is a well-known association in patients with von Hippel-Lindau disease. However, extra-adrenal pheochromocytoma or paraganglioma with this association is rare. We describe a patient with von Hippel-Lindau disease who presented with haematuria and was diagnosed to have a urinary bladder paraganglioma, which is an extremely rare tumour. Herein we report this case which, to the best of our knowledge, represents the first case highlighting the association of urinary bladder paraganglioma with von Hippel-Lindau disease.
嗜铬细胞瘤是冯·希佩尔-林道病患者中一种广为人知的关联疾病。然而，与这种关联相关的肾上腺外嗜铬细胞瘤或副神经节瘤却很罕见。我们描述了一名患有冯·希佩尔-林道病的患者，该患者出现血尿，被诊断患有膀胱副神经节瘤，这是一种极其罕见的肿瘤。在此，我们报告这一病例，据我们所知，这是首例突显膀胱副神经节瘤与冯·希佩尔-林道病关联的病例。
