Ophthalmology, Sri Sathya Sai Institute of Higher Medical Sciences Whitefield, Bangalore, Karnataka, India.
Smt Kanuri Santhamma Centre for Vitreo-Retinal Diseases, LV Prasad Eye Institute, Hyderabad, Telangana, India
BMJ Case Rep. 2022 Mar 23;15(3):e245907. doi: 10.1136/bcr-2021-245907.
A man in his 20s presented to the neurosurgery department 2 years ago with headache and blurred vision. He was diagnosed to have a suprasellar mass on neuroimaging. Best-corrected visual acuity in the right eye was 6/36 and that in the left eye was 6/60. Automated visual fields showed a temporal hemianopia in the right eye and an advanced field defect in the left eye. His hormonal profile was normal, and he underwent partial excision of suprasellar tumour, which was a histopathologically proven paraganglioma (PGL). Subsequently, the patient underwent radiotherapy and his vision and visual fields showed improvement. Follow-up examination 3 years later showed a left retinal capillary hemangioblastoma (RCH), which was treated with green laser photocoagulation, resulting in complete sclerosis. This case is unique because of the extremely rare coexistence of a sellar PGL and RCH, which to our knowledge has not been reported so far.
一位 20 多岁的男性患者于 2 年前因头痛和视力模糊就诊于神经外科。神经影像学检查诊断为鞍上肿块。右眼最佳矫正视力为 6/36，左眼为 6/60。自动视野检查显示右眼颞侧偏盲，左眼视野缺损严重。他的激素水平正常，接受了鞍上肿瘤的部分切除术，术后病理证实为副神经节瘤（PGL）。随后，患者接受了放疗，视力和视野均有所改善。3 年后的随访检查发现左侧视网膜毛细血管瘤（RCH），行绿光激光光凝治疗后完全硬化。本例独特之处在于罕见的鞍内 PGL 和 RCH 同时存在，据我们所知，目前尚未有相关报道。
