Hirayama Masaya, Komiya Tatsuhiko, Shimamoto Takeshi, Nonaka Michihito, Matsuo Takehiko, Shirakami Taku, Sugaya Atsushi, Fujimoto Haruka, Fujimoto Yasuyuki, Yano Atsushi
Department of Cardiovascular Surgery, Kurashiki Central Hospital, Kurashiki, Japan.
Kyobu Geka. 2020 Apr;73(4):307-311.
Primary pulmonary artery sarcoma is a very rare tumor. The prognosis of primary pulmonary artery sarcoma is extremely poor and it is reported as 1.5 months without treatment. Here we report our experience of surgical treatment of primary pulmonary artery sarcoma. A 66-year-old woman with a diagnosis of pulmonary sarcoma by chest computed tomography( CT) scan was referred to our hospital because of a loss of consciousness. An emergecy surgery was planned to eliminate the risk of sudden death. To avoid circulatory collapse, we placed her on extracorporeal bypass before anesthesia induction. The tumor extending from right ventricle outflow tract to bilateral pulmonary artery was removed and resected without leaving residual mass, but the surgical margin was positive, and adjuvant chemoradiotherapy was performed after discharge. In conclusion, surgical resection was succesfully conducted to avoid sudden death.
原发性肺动脉肉瘤是一种非常罕见的肿瘤。原发性肺动脉肉瘤的预后极差，据报道未经治疗的生存期为1.5个月。在此，我们报告我们对原发性肺动脉肉瘤的手术治疗经验。一名66岁女性因胸部计算机断层扫描（CT）诊断为肺肉瘤，因意识丧失转诊至我院。计划进行急诊手术以消除猝死风险。为避免循环衰竭，我们在麻醉诱导前将她置于体外循环。切除了从右心室流出道延伸至双侧肺动脉的肿瘤，且未残留肿块，但手术切缘阳性，出院后进行了辅助放化疗。总之，成功进行了手术切除以避免猝死。
