Department of Gastroenterology and Hepatology, "Victor Babeș" University of Medicine and Pharmacy, Timisoara, Romania.
Neuromed Diagnostic Imaging Center Timișoara, Romania.
Med Ultrason. 2021 May 20;23(2):235-237. doi: 10.11152/mu-2503. Epub 2020 Apr 23.
Primary biliary tract neuroendocrine tumors (NETs) are extremely rare tumors that account for 0.2-2% of all gastrointestinal neuroendocrine tumors. The typical presentation is with jaundice and other symptoms related to biliary obstruction.We present a case of right hepatic duct NET in a 27-year-old female patient, asymptomatic, presented for a routine ultrasound examination that revealed moderate dilatation of the intrahepatic biliary ducts and a 20 mm hyperechoic lesion in the right hepatic biliary duct. Additional imaging was performed with the presumptive diagnosis of cholangiocarcinoma. After surgery, the histopathological and immunohistochemical report was conclusive for the diagnosis of G2 well-differentiated NET.
原发性肝胆道神经内分泌肿瘤（NET）极为罕见，占所有胃肠道神经内分泌肿瘤的 0.2-2%。其典型表现为黄疸和其他与胆道梗阻相关的症状。我们报告一例 27 岁女性患者的右肝管 NET，患者无症状，因常规超声检查发现肝内胆管中度扩张和右肝管内 20mm 高回声病变而就诊。额外的影像学检查提示为胆管癌。手术后，组织病理学和免疫组织化学报告明确诊断为 G2 分化良好的 NET。
