Sahu Kananbala, Sirka Chandra Sekhar, Pradhan Swetalina, Rout Arpita Nibedita, Nayak Subhasini
Department of Dermatology, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India.
Pathology (Former Senior Resident S.C.B. Medical College), Cuttack, Odisha, India.
Indian Dermatol Online J. 2020 Mar 9;11(2):232-234. doi: 10.4103/idoj.IDOJ_100_19. eCollection 2020 Mar-Apr.
Pustular cutaneous vasculitis is a rare entity. Only handful cases are reported from all over the world. They typically present with painful pustules mainly over dorsum of hands and rarely on lower legs. We report a 50-year female who presented with painful pustules arranged in annular pattern predominantly distributed over lower limbs. Laboratory investigation ruled out any systemic associations. Histopathology was suggestive of pustular vasculitis. Final diagnosis of idiopathic pustular vasculitis was made. The patient was successfully treated with oral prednisolone and dapsone without any recurrence on follow up. It is the first report of annular morphological presentation of pustular vasculitis.
脓疱性皮肤血管炎是一种罕见的病症。全世界仅报道了少数病例。它们通常表现为主要在手背部出现疼痛性脓疱,很少出现在小腿上。我们报告了一名50岁女性,她出现疼痛性脓疱,呈环状分布,主要分布在下肢。实验室检查排除了任何系统性关联。组织病理学提示为脓疱性血管炎。最终诊断为特发性脓疱性血管炎。该患者口服泼尼松龙和氨苯砜治疗成功,随访无复发。这是脓疱性血管炎环状形态表现的首例报告。