McNeely M C, Jorizzo J L, Solomon A R, Schmalstieg F C, Cavallo T
J Am Acad Dermatol. 1986 May;14(5 Pt 2):939-44. doi: 10.1016/s0190-9622(86)70116-3.
Pustular cutaneous vasculitis results from a heterogeneous group of disorders characterized by pustules on purpuric bases. Although the cause of this group of conditions is diverse, the histopathologic picture of the lesions is the same, showing a Sweet's-like or leukocytoclastic vasculitis. These distinctive lesions may occur in patients with Behçet's syndrome, bowel-associated dermatosis-arthritis syndrome, or chronic gonococcemia. We describe, for the first time, a patient with primary idiopathic cutaneous pustular vasculitis. This patient had evidence of both circulating immune complexes and serum enhancement of neutrophil migration. Extensive evaluation failed to reveal any underlying systemic disease. A classification of the pustular vasculitides is proposed.
脓疱性皮肤血管炎由一组异质性疾病引起，其特征为紫癜性基底上出现脓疱。尽管这组病症的病因多种多样，但病变的组织病理学表现相同，显示为Sweet样或白细胞破碎性血管炎。这些独特的病变可能发生在白塞病、肠道相关皮肤病-关节炎综合征或慢性淋菌血症患者中。我们首次描述了一名原发性特发性皮肤脓疱性血管炎患者。该患者有循环免疫复合物和血清中性粒细胞趋化性增强的证据。广泛评估未能发现任何潜在的全身性疾病。本文提出了脓疱性血管炎的分类。
