Zhao J
Gulou Hospital, Nanjing.
Zhonghua Zhong Liu Za Zhi. 1988 Sep;10(5):395-6.
Extramedullary plasmacytoma (EMP), being different from multiple myeloma, is very rare. One case of primary EMP of small intestine and review of literature are presented. The patient, 69-year-old male, was admitted because of left lower abdominal pain and anemia. A mass, table-tennis in size, was palpated. Intestinal obstruction was found by plain X-ray film. It was diagnosed as EMP of small intestine by pathology after exploratory celiotomy. Immunohistochemical stain showed that intracytoplasmic immunoglobulin was monoclonal IgG. Lambda. The blood Bence-Jones protein and bone marrow puncture were negative. The patient received chemotherapy after operation and was followed for two years giving satisfactory result. The pathogenesis, clinical feature, diagnostic criteria and treatment are discussed.
髓外浆细胞瘤(EMP)与多发性骨髓瘤不同,非常罕见。本文报告1例原发性小肠EMP并进行文献复习。患者为69岁男性,因左下腹痛和贫血入院。触诊发现一个乒乓球大小的肿块。腹部平片显示肠梗阻。经剖腹探查术后病理诊断为小肠EMP。免疫组化染色显示胞浆内免疫球蛋白为单克隆IgG、λ。血本-周蛋白及骨髓穿刺均为阴性。患者术后接受化疗,随访两年效果满意。文中讨论了其发病机制、临床特征、诊断标准及治疗方法。