Department of Plastic and Reconstructive Surgery, Mie University Hospital, Tsu, Mie, Japan.
Department of Plastic and Reconstructive Surgery, Mie University Hospital, Tsu, Mie, Japan.
J Vasc Surg Venous Lymphat Disord. 2021 Mar;9(2):499-503. doi: 10.1016/j.jvsv.2020.05.017. Epub 2020 Jun 4.
Large abdominal lymphatic malformations (LMs) are rare and may occasionally cause life-threatening illness, especially when they involve the central lymphatic system, lumbar trunks, cisterna chyli, thoracic duct, and their major tributaries, forming complex lymphatic anomalies. These LMs are often accompanied by chylous leak in various locations, and treatment remains challenging. We report a case of large abdominal LM with chylous ascites, protein-losing enteropathy, vaginal chylous leak, and lower limb lymphedema successfully treated with microsurgical intra-abdominal lymphovenous anastomosis and discuss the technical details of the procedure.
巨大的腹部淋巴管畸形（LM）较为罕见，有时可能会导致危及生命的疾病，尤其是当它们涉及中央淋巴系统、腰干、乳糜池、胸导管及其主要分支，形成复杂的淋巴畸形时。这些 LM 常伴有不同部位的乳糜漏，治疗仍然具有挑战性。我们报告了一例巨大的腹部 LM 合并乳糜性腹水、蛋白丢失性肠病、阴道乳糜漏和下肢淋巴水肿，成功地接受了显微外科腹腔内淋巴静脉吻合术治疗，并讨论了该手术的技术细节。
