Costa Adriano C, Santa-Cruz Fernando, Guimarães Henrique, Paz Alexandre R, Costa Eduardo A C, Figueiredo José-Luiz, Ferraz Álvaro A B
Oncological Surgery Unit, Napoleão Laureano Hospital, João Pessoa, PB, Brazil; Department of Surgery, Federal University of Pernambuco, Recife, PE, Brazil.
School of Medicine, Federal University of Pernambuco, Recife, PE, Brazil.
Int J Surg Case Rep. 2020;72:1-4. doi: 10.1016/j.ijscr.2020.05.057. Epub 2020 May 30.
Primary hepatic neuroendocrine tumors (PHNETs) are extremely rare, having less than 200 cases reported in the literature.
A 51-year-old woman presenting with mild intensity sharp pain in the upper abdomen that started 4 years ago. Preoperative Magnetic Resonance Imaging (MRI) suggested hepatocellular adenoma. Surgical exploration found a tumor occupying the whole segment IV of the liver, therefore a left hepatectomy was performed. Pathology and immunohistochemistry indicated to be a low-grade neuroendocrine tumor of the liver. The patient is enjoying a good quality of life, free of disease, presenting no signs of recurrence nor metastases 12 months after the procedure.
The clinical presentation of PHNETs is non-specific and its radiologic features are intensely diversified, frequently leading to misdiagnosis of other hepatic neoplasms.
原发性肝神经内分泌肿瘤（PHNETs）极为罕见，文献报道的病例不足200例。
一名51岁女性，4年前开始出现上腹部轻度锐痛。术前磁共振成像（MRI）提示肝细胞腺瘤。手术探查发现一个肿瘤占据肝脏整个IV段，因此进行了左肝切除术。病理及免疫组化显示为肝脏低级别神经内分泌肿瘤。患者生活质量良好，无疾病困扰，术后12个月未出现复发及转移迹象。
PHNETs的临床表现无特异性，其影像学特征高度多样化，常导致误诊为其他肝脏肿瘤。
