Martin Felicity C, Yang Linda S, Fehily Sasha R, D'Souza Basil, Lim Allan, McKelvie Penelope A
Department of Gastroenterology St Vincent's Hospital Fitzroy Victoria Australia.
Department of Colorectal Surgery St Vincent's Hospital Fitzroy Victoria Australia.
JGH Open. 2019 Dec 27;4(3):345-350. doi: 10.1002/jgh3.12297. eCollection 2020 Jun.
In 1991, Genta and Haggitt described four patients with segmental ischemic colitis caused by idiopathic myointimal hyperplasia in the small mesenteric veins (IMHMV). There are now 33 published cases of IMHMV in the literature; however, this condition is still sufficiently rare that it poses a diagnostic challenge to pathologists and clinicians and is often clinically or histologically confused with inflammatory bowel disease (IBD) or ischemic colitis. IMHMV is characterized by intimal smooth muscle hyperplasia resulting in thickened small and medium-sized mesenteric veins (with arterial sparing). Clinically, it presents with symptoms that mimic IBD, such as bloody diarrhea, abdominal pain, and weight loss. Surgical resection appears to be curative. The present case describes a 63-year-old Vietnamese man with cardiovascular risk factors who was diagnosed with IMHMV after many months of severe symptoms. A review of the current literature follows the case report.
1991年，根塔（Genta）和哈吉特（Haggitt）描述了4例由特发性肌内膜增生累及小肠系膜静脉（IMHMV）导致节段性缺血性结肠炎的患者。目前文献中已发表33例IMHMV病例；然而，这种疾病仍然极为罕见，给病理学家和临床医生带来了诊断挑战，并且在临床或组织学上常与炎症性肠病（IBD）或缺血性结肠炎相混淆。IMHMV的特征是内膜平滑肌增生，导致中小肠系膜静脉增厚（不累及动脉）。临床上，它表现出类似IBD的症状，如血性腹泻、腹痛和体重减轻。手术切除似乎可治愈。本病例描述了一名63岁有心血管危险因素的越南男子，在出现严重症状数月后被诊断为IMHMV。病例报告之后是对当前文献的综述。
