Han Ga-Ram, Mehrotra Anchit P, Gomez Adam J, Romanucci Eric, Halpern Vivienne J
Department of General Surgery, Mayo Clinic Arizona, Phoenix, AZ.
Department of General Surgery, Banner University Medical Center-Phoenix, The University of Arizona, Phoenix, AZ.
J Vasc Surg Cases Innov Tech. 2022 Jul 6;8(3):520-533. doi: 10.1016/j.jvscit.2022.05.014. eCollection 2022 Sep.
Only 50 cases of idiopathic myointimal hyperplasia of the mesenteric veins (IMHMV) have been reported since 1991 when it was first described. This rare etiology for chronic colonic ischemia is often debilitating to the patient's quality of life, and no effective medical treatment is available. IMHMV is frequently confused with inflammatory bowel disease because the most common presenting symptoms include abdominal pain, diarrhea, and hematochezia. Surgical resection is curative; however, the diagnosis is rarely reached preoperatively. In the present report, we have described the seventh patient with a diagnosis of IMHMV before surgery and included a literature review to help clinicians recognize this condition.
自1991年首次描述以来,仅报告了50例肠系膜静脉特发性肌内膜增生(IMHMV)。这种慢性结肠缺血的罕见病因常常损害患者的生活质量,并且没有有效的药物治疗方法。IMHMV常与炎症性肠病相混淆,因为最常见的症状包括腹痛、腹泻和便血。手术切除可治愈;然而,术前很少能做出诊断。在本报告中,我们描述了第七例术前诊断为IMHMV的患者,并进行了文献综述以帮助临床医生认识这种疾病。