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肾脏巨大双侧血管平滑肌脂肪瘤。

Giant bilateral angiomyolipoma of the kidney.

机构信息

Maulana Azad Medical College, New Delhi, India.

出版信息

Ann R Coll Surg Engl. 2021 Jun;103(6):e184-e188. doi: 10.1308/rcsann.2020.7036. Epub 2021 May 6.

Abstract

Angiomyolipoma is a benign solid renal neoplasm. A giant angiomyolipoma is more than 10cm by size, but it can grow to huge proportions. Our case appears to be the third largest angiomyolipoma and the largest among bilateral giant renal angiomyolipoma in the indexed literature. A 26-year-old man presented with large right abdominal swelling for the past three years, which was occupying his right flank and iliac region, extending beyond the midline. Computed tomography of the abdomen revealed a large well-defined mass in the right side of the abdomen, crossing the midline and measuring 35 × 20 × 12cm. The left kidney showed a similar fatty lesion of 14 × 6cm. The findings were consistent with angiomyolipoma. Further evaluation for tuberous sclerosis by magnetic resonance imaging the brain demonstrated multiple subependymal nodules. Giant renal angiomyolipoma is an uncommon tumour with bilateral giant angiomyolipoma being a rare entity. Preoperative embolisation helps in reducing size of the tumour. In case of giant and bilateral angiomyolipoma, evaluation for tuberous sclerosis should always be done.

摘要

血管平滑肌脂肪瘤是一种良性的肾脏实体肿瘤。巨血管平滑肌脂肪瘤的大小超过 10cm,但它可以长到巨大的比例。我们的病例似乎是第三大血管平滑肌脂肪瘤,也是索引文献中双侧巨大肾血管平滑肌脂肪瘤中最大的一个。一名 26 岁男性因过去三年右侧腹部肿胀就诊,肿胀占据了他的右侧腰部和髂区,超出了中线。腹部 CT 显示右侧腹部有一个大而清晰的肿块,穿过中线,大小为 35×20×12cm。左肾有一个类似的脂肪病变,大小为 14×6cm。这些发现与血管平滑肌脂肪瘤一致。对脑部磁共振成像进行结节性硬化症的进一步评估显示多个室管膜下结节。巨大的肾血管平滑肌脂肪瘤是一种不常见的肿瘤,双侧巨大的肾血管平滑肌脂肪瘤则是一种罕见的实体瘤。术前栓塞有助于缩小肿瘤的大小。对于巨大和双侧的血管平滑肌脂肪瘤,应始终进行结节性硬化症的评估。

相似文献

1
Giant bilateral angiomyolipoma of the kidney.肾脏巨大双侧血管平滑肌脂肪瘤。
Ann R Coll Surg Engl. 2021 Jun;103(6):e184-e188. doi: 10.1308/rcsann.2020.7036. Epub 2021 May 6.
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Huge bilateral renal angiomyolipoma.巨大双侧肾血管平滑肌脂肪瘤。
BMJ Case Rep. 2013 Jan 25;2013:bcr2012007418. doi: 10.1136/bcr-2012-007418.

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Imaging of tuberous sclerosis complex: a pictorial review.结节性硬化症的影像学:图文综述
Radiol Bras. 2017 Jan-Feb;50(1):48-54. doi: 10.1590/0100-3984.2016.0020.
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Update on the Diagnosis and Management of Renal Angiomyolipoma.肾血管平滑肌脂肪瘤的诊断和治疗进展。
J Urol. 2016 Apr;195(4 Pt 1):834-46. doi: 10.1016/j.juro.2015.07.126. Epub 2015 Nov 21.

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