幼年型大疱性系统性红斑狼疮 - 病例报告。
Juvenile bullous systemic lupus erythematosus - case report.
机构信息
Hospital Garcia de Orta.
出版信息
Acta Reumatol Port. 2020 Jan-Mar;45(1):74-75.
PMID:32608382
Abstract
Bullous systemic lupus erythematosus (BSLE) is a rare autoimmune subepidermal blistering disease, with few cases described in childhood. We report a case of bullous systemic lupus erythematosus refractory to corticosteroid therapy in a 16-year-old female who was successfully treated with low dose dapsone. We highlight the rarity and the relevance of skin biopsy for a correct diagnosis of BSLE.
摘要
大疱性系统性红斑狼疮（BSLE）是一种罕见的自身免疫性表皮下疱病，儿童期病例较少。我们报告了一例 16 岁女性 BSLE 患者，对皮质类固醇治疗无效，用小剂量氨苯砜治疗成功。我们强调了皮肤活检对于正确诊断 BSLE 的罕见性和相关性。
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