University of Torino, Orbassano, Italy.
San Luigi Gonzaga Hospital, Orbassano, Italy.
J Investig Med High Impact Case Rep. 2020 Jan-Dec;8:2324709620939802. doi: 10.1177/2324709620939802.
Progressive multifocal leukoencephalopathy (PML) is a serious infective disease of the central nervous system that may occur in case of severe immunosuppression or after some treatment for multiple sclerosis (MS) with natalizumab, dimethyl fumarate, and fingolimod. In these case reports, we highlight the importance of differential diagnosis between PML and MS lesions in order to provide rapidly the best treatment option, by discussing the finding of brain (magnetic resonance imaging) MRI suggestive for PML in 2 MS patients, one treated with dimethyl fumarate and the other during natalizumab withdrawal. In both cases, although brain MRI was highly suggestive for PML, the detection of John Cunningham virus-DNA copies in cerebrospinal fluid resulted in negative result. These case reports illustrate the diagnostic process in case of suspected PML, as both patients were diagnosed with suspected PML during a routine brain MRI control, and highlights the importance of providing a strict brain MRI follow-up during dimethyl fumarate treatment, although only a few cases of PML during this therapy have been detected, and during natalizumab suspension phase. In clinical practice, in case of a radiologically suspected case of PML, although not confirmed by the cerebrospinal fluid analysis, the best approach could be to perform a close radiological and clinical monitoring before starting a new MS therapy.
进行性多灶性白质脑病(PML)是一种严重的中枢神经系统感染性疾病,可能发生于严重免疫抑制或使用那他珠单抗、富马酸二甲酯和芬戈莫德治疗多发性硬化症(MS)之后。在这些病例报告中,我们强调了在 PML 和 MS 病变之间进行鉴别诊断的重要性,以便通过讨论在 2 名接受富马酸二甲酯和另 1 名接受那他珠单抗停药治疗的 MS 患者中发现的脑(磁共振成像)MRI 提示 PML 的结果,迅速提供最佳治疗方案。在这两种情况下,尽管脑 MRI 高度提示 PML,但脑脊液中 John Cunningham 病毒-DNA 拷贝的检测结果为阴性。这些病例报告说明了在疑似 PML 的情况下的诊断过程,因为这两名患者在常规脑 MRI 检查中被诊断为疑似 PML,并强调了在富马酸二甲酯治疗期间进行严格的脑 MRI 随访的重要性,尽管在此治疗期间仅检测到少数 PML 病例,以及在那他珠单抗停药期间。在临床实践中,对于疑似 PML 的放射学病例,尽管脑脊液分析未得到证实,但在开始新的 MS 治疗之前,进行密切的放射学和临床监测可能是最佳方法。