Sothornwit Jen, Temtanakitpaisan Teerayut, Aue-Aungkul Apiwat, Likitdee Naratassapol, Kleebkaow Pilaiwan
Department of Obstetrics and Gynecology, Faculty of Medicine, Khon Kaen University, Thailand.
Gynecol Oncol Rep. 2020 Jul 15;33:100609. doi: 10.1016/j.gore.2020.100609. eCollection 2020 Aug.
Extragastrointestinal stromal tumors (EGISTs) arise from atypical sites, such as the omentum, mesentery, retroperitoneal space, urinary bladder, or rectovaginal septum, and account for fewer than 10% of gastrointestinal stromal tumors (GISTs). Most EGISTs are asymptomatic at the time of diagnosis, due to the fact that they rarely cause symptoms until they grow to greater than 10 cm in diameter. Common presenting symptoms are a feeling of vaginal fullness and increased urinary frequency. Cases described in previous reports have been treated with surgery with or without targeted therapy. Here we report an unusual case of an EGIST at the rectovaginal septum presenting with excessive vaginal bleeding and acute arterial occlusion. This rectovaginal mass was successfully removed using the abdominoperineal approach and did not require targeted therapy.
胃肠道外间质瘤（EGIST）起源于非典型部位，如大网膜、肠系膜、腹膜后间隙、膀胱或直肠阴道隔，占胃肠道间质瘤（GIST）的比例不到10%。大多数EGIST在诊断时无症状，因为它们很少引起症状，直到直径超过10厘米。常见的症状是阴道胀满感和尿频增加。既往报道的病例采用手术治疗，联合或不联合靶向治疗。在此，我们报告一例罕见的直肠阴道隔EGIST病例，表现为阴道大量出血和急性动脉闭塞。该直肠阴道肿块采用腹会阴联合入路成功切除，无需靶向治疗。
