Hospital Sultanah Nora Ismail, Department of Internal Medicine, Johor, Malaysia.
Hospital Lahad Datu, Department of Internal Medicine, Sabah, Malaysia.
Med J Malaysia. 2020 Jul;75(4):452-454.
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare inherited cardiomyopathy characterised by right ventricular dysfunction, ventricular arrhythmias and increased risk of sudden cardiac death. Due to the replacement of myocardium with fibro-fatty and fibrous tissue, patients with ARVC are prone to develop ventricular tachycardia. Histologically, it is often reported as the 'triangle of dysplasia' involving the inflow tract, outflow tract and apex of the right ventricle.2 We describe a 20-years-old patient who collapsed during a futsal match and was subsequently diagnosed to have ARVC with a right ventricular thrombus from cardiac magnetic resonance imaging.
致心律失常性右室心肌病（ARVC）是一种罕见的遗传性心肌病，其特征为右心室功能障碍、室性心律失常和猝死风险增加。由于心肌被纤维脂肪和纤维组织取代，ARVC 患者易发生室性心动过速。组织学上，它通常被报道为涉及右心室流入道、流出道和心尖的“发育不良三角”。2 我们描述了一位 20 岁的患者，他在一场五人制足球比赛中晕倒，随后通过心脏磁共振成像诊断为 ARVC 合并右心室血栓形成。
